不完全川崎病的诊治现状

:(2003-1018):100034,:(Emai:ljunbaodu1@1261com)##张清友杜军保(Kawasakidisease,KD),[1]1967KawasakiTomisaku,,KDKD1318%[2],1914%KD(atypicalorincomplete)[3],KDKDKD\5d54[4]KD,KD,\5d,523,Stevens-JohnsonEpstein-Barr(EB),KD,,/(incomplete)0KD/(atypical)0KD[5]KDKD,KD,10%~36%[6],1914%[3],Genizi[7],316,28%KD,14%10d(intravenousimmunoglobulin,IVIG),85%,7KD,,,82%;KD,,65%[4,7]Witt[8],127KD46KD,IVIG1214d,IVIG812dKD20%,7%KDKD,KD,,,KDKD,KD515%,KD[2]KD,KDKD,KD[6-8],KD,KD,,C-(CRP)(ESR),10d,KD[1](BCG),KD[9](brainnatriureticpeptide,BNP)KD,,KD[10,11](theAmericanAcademyofPediatrics,AAP)(theAmericanHeartAssociation,AHA)KD,5d2~3KD,[1,12],ESRCRPESR40mm/hCRP\30mg/L,KD,IVIGKD,5dESRCRPIVIG,2004AAPAHAKD[1]:\5d,23,KD;KD,;,;KD,,;CRP30mg/LESR40mm/h,,#339#20065445ChinJPediatr,May2006,Vol44,No152d,KD;,,KD;,(ultroechocardiography,UCG),:(LAD)(RCA)z\215;;33:(lacktapering)LADRCAz2~215KD,KDCRP\30mg/L()ESR\40mm/h,,[30g/L7d\450@109/L\15@109/L\10/HP,\3,KD,IVIG,UCG;3,UCG,UCG,KD,;UCG,,,KD;,UCG,KD,2:(1)KD,,,,,;(2)[6,\7d,,,KD,[13]KDKD,KD,KDKDStevens-JohnsonEB[14],,IgM;A,,,Steven-Johnson(),KD,KDKD,IVIG[5],EB[9],EB[15]EBIgMEB,KD[16],KDESR(56mm/hvs42mm/h),,KD[17],,KD,KDKDKDKD,IVIG,[1],KD,KD,11d,KD,,,12~14d,,[CRP()ESR],IVIG[1,5]12~14d,,,,2,,[5]1NewburgerJW,TakahashiM,GerberMA,eta.lDiagnosis,treatment,andlong-termmanagementofKawasakidisease:astatementforHealthProfessionalsfromtheCommitteeonRheumaticFever,EndocarditisandKawasakiDisease,CouncilonCardiovascularDiseaseintheYoung,AmericanHeartAssociation.Circulation,2004,110:2747-2771.2SonobeT,AsoS,ImadaY,eta.lTheincidenceofcoronaryarteryabnormalitiesinincompleteKawasakidisease.PediatrRes,2003,53:164.3琍,林毅,苏英姿,等.283例川崎病的临床分析.中华儿科杂,2004,42:609-612.4AyuswaM,SonobeT,UemuraS,eta.lRevisionofdiagnosticguidelinesforKawasakidisease(the5threvisededition).PediatrInt,2005,47:232-234.5FreemanAF,ShulmanST.IssuesinthediagnosisofKawasakidisease.ProgPediatrCardio,l2004,19:123-128.6RowleyAH.Incomplete(atypical)Kawasakidisease.PediatrInfectDisJ,2002,21:563-565.7GeniziJ,MironD,SpiegelR,eta.lKawasakidiseaseinveryyounginfants:highprevalenceofatypicalpresentationandcoronaryarteritis.ClinPediatr,2003,42:263-267.8WittMT,MinichLL,BohnsackJF,eta.lKawasakidisease:more#340#20065445ChinJPediatr,May2006,Vol44,No15patientsarebeingdiagnosedwhodonotmeetAmericanHeartAssociationcriteria.Pediatrics,1999,104:e10.9..,2002,40:65-67.10KawamuraT,WagoM,KawaguchiH,eta.lPlasmabrainnatriureticpeptideconcentrationsinpatientswithKawasakidisease.PediatrInt,2000,42:241-248.11KurotobiS,KawakamiN,ShimizuK,eta.lBrainnatriureticpeptideasahormonalmarkerofventriculardiastolicdysfunctioninchildrenwithKawasakidisease.PediatrCardio,l2005,26:425-430.12ShulmanST,RowleyAH.AdvancesinKawasakidisease.EurJPediatr,2004,163:285-291.13BaumerJH.Kawasakidisease:whattodowithincompletecases?ArchDisChildEducPractEdu,2005,90:ep102-ep104.14RowleyAH,ShumanST.Kawasakisyndrome.PediatrClinNorthAm,1999,46:313-329.15,玗,陈洁.儿童EB病毒感染首发症状及相关疾病谱.,2004,42:20-22.16BaronSR,PontrelliLR,KrilovLR.ThedifferentiationofclassicKawasakidiseaseatypicalKawasakidisease,andacuteadenoviralinfection.ArchPediatrAdoleseMed,2000,154:453-456.17RochollC,GerberK,DalyJ,eta.lAdenovirusinfectionsinchildren:theimpactofrapiddiagnosis.Pediatrics,2004,113:e51-56.(:2006-01-04)(:)####第三届中国国际先天性心脏病介入治疗暨手术演示学术会议征文通知(会议将延期召开)565656/0,109~11:(1);(2);(3);(4),,,1.:(1)();(2)();(3),;(4);(5);(6)();(7)();(8);(9)(,);(10)();(11);(12)2.:(1);(2)3000~4000,;1,800~1000,:;(3),,;(4),(Word)(5),3./0,,,Ñ4.:2006610();:4256,:100710;/0:010-85158217,010-85158220;:010-85158359Emai:[e-mail]#341#20065445ChinJPediatr,May2006,Vol44,No15